Annotation Detail

Information
Associated Genes
FECH
Associated Variants
FECH p.Phe423Ser (p.F423S) ( ENST00000262093.11, ENST00000382873.8, ENST00000652755.1 )
FECH p.Phe423Ser (p.F423S) ( ENST00000262093.11, ENST00000382873.8, ENST00000652755.1 )
Associated Disease
Protoporphyria, erythropoietic, 1
Source Database
ClinVar
Description
NM_000140.5(FECH):c.1250T>C (p.Phe417Ser) AND Protoporphyria, erythropoietic, 1
ClinVar Allele ID
15590
ClinVar RefSeq Alternation Syntax
NM_001371094.1:c.1151T>C
ClinVar RefSeq Alternation Syntax
NM_000140.5:c.1250T>C
ClinVar RefSeq Alternation Syntax
NM_001012515.4:c.1268T>C
ClinVar RefSeq Alternation Syntax
NM_001371095.1:c.1034T>C
ClinVar RefSeq Alternation Syntax
NM_001374778.1:c.1190T>C
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
1992-06-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000000581
ClinVar Disease
Protoporphyria, erythropoietic, 1
Observed Origin Sample
germline
Pubmed
1376018
Drugs