Annotation Detail

Information
Associated Genes
FECH
Associated Variants
FECH c.1095+1G>A ( ENST00000262093.11, ENST00000382873.8, ENST00000652755.1 )
FECH c.1095+1G>A ( ENST00000262093.11, ENST00000382873.8, ENST00000652755.1 )
Associated Disease
Protoporphyria, erythropoietic, 1
Source Database
ClinVar
Description
NM_000140.5(FECH):c.1077+1G>A AND Protoporphyria, erythropoietic, 1
ClinVar Allele ID
15591
ClinVar RefSeq Alternation Syntax
NM_001371094.1:c.978+1G>A
ClinVar RefSeq Alternation Syntax
NM_001371095.1:c.861+1G>A
ClinVar RefSeq Alternation Syntax
NM_001012515.4:c.1095+1G>A
ClinVar RefSeq Alternation Syntax
NM_000140.5:c.1077+1G>A
ClinVar RefSeq Alternation Syntax
NM_001374778.1:c.1077+1G>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
1993-05-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000000582
ClinVar Disease
Protoporphyria, erythropoietic, 1
Observed Origin Sample
germline
Pubmed
8500787
Pubmed
3940245
Drugs