Annotation Detail

Information
Associated Genes
FECH
Associated Variants
FECH c.1155+3A>G ( ENST00000262093.11, ENST00000382873.8, ENST00000652755.1 )
FECH c.1155+3A>G ( ENST00000262093.11, ENST00000382873.8, ENST00000652755.1 )
Associated Disease
Protoporphyria, erythropoietic, 1
Source Database
ClinVar
Description
NM_000140.5(FECH):c.1137+3A>G AND Protoporphyria, erythropoietic, 1
ClinVar Allele ID
15592
ClinVar RefSeq Alternation Syntax
NM_001371094.1:c.1038+3A>G
ClinVar RefSeq Alternation Syntax
NM_001012515.4:c.1155+3A>G
ClinVar RefSeq Alternation Syntax
NM_001374778.1:c.1078-466A>G
ClinVar RefSeq Alternation Syntax
NM_001371095.1:c.921+3A>G
ClinVar RefSeq Alternation Syntax
NM_000140.5:c.1137+3A>G
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
1994-06-04
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000000583
ClinVar Disease
Protoporphyria, erythropoietic, 1
Observed Origin Sample
germline
Pubmed
7910885
Pubmed
3047929
Drugs