Annotation Detail

Information
Associated Genes
NLRP7
Associated Variants
NLRP7 p.Leu398Arg (p.L398R) ( ENST00000328092.9, ENST00000340844.6, ENST00000588756.5, ENST00000590030.5, ENST00000592784.6 )
NLRP7 p.Leu398Arg (p.L398R) ( ENST00000328092.9, ENST00000340844.6, ENST00000588756.5, ENST00000590030.5, ENST00000592784.6 )
Associated Disease
Hydatidiform mole, recurrent, 1
Source Database
ClinVar
Description
NM_001127255.2(NLRP7):c.1193T>G (p.Leu398Arg) AND Hydatidiform mole, recurrent, 1
ClinVar Allele ID
16631
ClinVar RefSeq Alternation Syntax
NM_001127255.2:c.1193T>G
ClinVar RefSeq Alternation Syntax
NM_139176.4:c.1193T>G
ClinVar RefSeq Alternation Syntax
NM_206828.4:c.1193T>G
ClinVar RefSeq Alternation Syntax
NM_001405531.1:c.1193T>G
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2009-08-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000001659
ClinVar Disease
Hydatidiform mole, recurrent, 1
Observed Origin Sample
germline
Observed Origin Sample
not provided
Pubmed
12471053
Pubmed
19246479
Drugs