Annotation Detail

Information
Associated Genes
CAV3 OXTR
Associated Variants
CAV3 p.Thr78Met (p.T78M) ( ENST00000343849.3, ENST00000397368.2 )
CAV3 p.Thr78Met (p.T78M) ( ENST00000343849.3, ENST00000397368.2 )
Associated Disease
Long QT syndrome 2/9, digenic
Source Database
ClinVar
Description
NM_033337.3(CAV3):c.233C>T (p.Thr78Met) AND Long QT syndrome 2/9, digenic
ClinVar Allele ID
23332
ClinVar RefSeq Alternation Syntax
NM_033337.3:c.233C>T
ClinVar RefSeq Alternation Syntax
NM_001234.5:c.233C>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2007-02-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000008791
ClinVar Disease
Long QT syndrome 2/9, digenic
Observed Origin Sample
germline
Pubmed
17275750
Pubmed
15580566
Pubmed
17060380
Drugs