Annotation Detail

Information
Associated Genes
G6PC1
Associated Variants
G6PC1 p.Arg83Cys (p.R83C) ( ENST00000592383.5, ENST00000253801.7, ENST00000585489.1 )
G6PC1 p.Arg83Cys (p.R83C) ( ENST00000253801.7, ENST00000585489.1, ENST00000592383.5 )
Associated Disease
Glycogen storage disease due to glucose-6-phosphatase deficiency type IA
Source Database
ClinVar
Description
NM_000151.4(G6PC1):c.247C>T (p.Arg83Cys) AND Glycogen storage disease due to glucose-6-phosphatase deficiency type IA
ClinVar Allele ID
27037
ClinVar RefSeq Alternation Syntax
NM_001270397.2:c.247C>T
ClinVar RefSeq Alternation Syntax
NM_000151.4:c.247C>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2024-01-29
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000012778
ClinVar Disease
Glycogen storage disease due to glucose-6-phosphatase deficiency type IA
Observed Origin Sample
germline
Observed Origin Sample
inherited
Observed Origin Sample
unknown
Pubmed
7573034
Pubmed
8734807
Pubmed
2172641
Pubmed
8182131
Pubmed
9332655
Pubmed
8211187
Pubmed
15316959
Drugs