Annotation Detail

Information
Associated Genes
KRT5
Associated Variants
KRT5 p.Pro25Leu (p.P25L) ( ENST00000252242.9 )
KRT5 p.Pro25Leu (p.P25L) ( ENST00000252242.9 )
Associated Disease
epidermolysis bullosa simplex with mottled pigmentation
Source Database
ClinVar
Description
NM_000424.4(KRT5):c.74C>T (p.Pro25Leu) AND Epidermolysis bullosa simplex with mottled pigmentation
ClinVar Allele ID
29687
ClinVar RefSeq Alternation Syntax
NM_000424.4:c.74C>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2010-11-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000015754
ClinVar Disease
Epidermolysis bullosa simplex with mottled pigmentation
Observed Origin Sample
germline
Observed Origin Sample
unknown
Pubmed
2476664
Pubmed
8799157
Pubmed
6457621
Pubmed
20923750
Pubmed
11167681
Pubmed
10494094
Pubmed
421361
Pubmed
9129237
Pubmed
16581562
Drugs