Annotation Detail

Information
Associated Genes
IMPDH1
Associated Variants
IMPDH1 p.Asp311Asn (p.D311N) ( ENST00000338791.11, ENST00000348127.11, ENST00000354269.9, ENST00000419067.6, ENST00000470772.5, ENST00000480861.5, ENST00000496200.5 )
IMPDH1 p.Asp311Asn (p.D311N) ( ENST00000338791.11, ENST00000348127.11, ENST00000354269.9, ENST00000419067.6, ENST00000470772.5, ENST00000480861.5, ENST00000496200.5 )
Associated Disease
retinitis pigmentosa 10
Source Database
ClinVar
Description
NM_000883.4(IMPDH1):c.931G>A (p.Asp311Asn) AND Retinitis pigmentosa 10
ClinVar Allele ID
29873
ClinVar RefSeq Alternation Syntax
NM_183243.3:c.823G>A
ClinVar RefSeq Alternation Syntax
NM_001142575.2:c.601G>A
ClinVar RefSeq Alternation Syntax
NM_000883.4:c.931G>A
ClinVar RefSeq Alternation Syntax
NM_001102605.2:c.901G>A
ClinVar RefSeq Alternation Syntax
NM_001142574.2:c.661G>A
ClinVar RefSeq Alternation Syntax
NM_001304521.2:c.724G>A
ClinVar RefSeq Alternation Syntax
NM_001142573.2:c.676G>A
ClinVar RefSeq Alternation Syntax
NM_001142576.2:c.832G>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2021-04-08
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000015959
ClinVar Disease
Retinitis pigmentosa 10
Observed Origin Sample
germline
Pubmed
15851576
Pubmed
16671097
Pubmed
11875050
Drugs