Annotation Detail

Information
Associated Genes
CFH
Associated Variants
ENSG00000289697 p.Glu1172Ter (p.E1172*), CFH p.Glu1172Ter (p.E1172*) ( ENST00000695984.1, ENST00000695981.1, ENST00000695974.1, ENST00000695971.1, ENST00000695976.1, ENST00000367429.9, ENST00000695970.1, ENST00000696028.1, ENST00000696027.1, ENST00000696029.1 )
ENSG00000289697 p.Glu1172Ter (p.E1172*), CFH p.Glu1172Ter (p.E1172*) ( ENST00000367429.9, ENST00000695970.1, ENST00000695971.1, ENST00000695974.1, ENST00000695976.1, ENST00000695981.1, ENST00000695984.1, ENST00000696027.1, ENST00000696028.1, ENST00000696029.1 )
Associated Disease
Hemolytic uremic syndrome, atypical, susceptibility to, 1
Source Database
ClinVar
Description
NM_000186.4(CFH):c.3514G>T (p.Glu1172Ter) AND Hemolytic uremic syndrome, atypical, susceptibility to, 1
ClinVar Allele ID
31598
ClinVar RefSeq Alternation Syntax
NM_000186.4:c.3514G>T
Clinical Significance Description
risk factor
Clinical Significance Last Update
2003-04-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000018027
ClinVar Disease
Hemolytic uremic syndrome, atypical, susceptibility to, 1
Observed Origin Sample
germline
Pubmed
12697737
Drugs