Annotation Detail

Information
Associated Genes
ERCC2
Associated Variants
ERCC2 p.Gln726Ter (p.Q726*) ( ENST00000391944.8, ENST00000391945.10, ENST00000684407.1 )
ERCC2 p.Gln726Ter (p.Q726*) ( ENST00000391944.8, ENST00000391945.10, ENST00000684407.1 )
Associated Disease
Xeroderma pigmentosum, group D
Source Database
ClinVar
Description
NM_000400.4(ERCC2):c.2176C>T (p.Gln726Ter) AND Xeroderma pigmentosum, group D
ClinVar Allele ID
31819
ClinVar RefSeq Alternation Syntax
NM_000400.4:c.2176C>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
1994-10-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000018269
ClinVar Disease
Xeroderma pigmentosum, group D
Observed Origin Sample
germline
Pubmed
7849702
Drugs