Annotation Detail

Information
Associated Genes
ERCC2
Associated Variants
ERCC2 p.Gly713Arg (p.G713R) ( ENST00000391944.8, ENST00000391945.10, ENST00000684407.1 )
ERCC2 p.Gly713Arg (p.G713R) ( ENST00000391944.8, ENST00000391945.10, ENST00000684407.1 )
Associated Disease
Trichothiodystrophy 1, photosensitive
Source Database
ClinVar
Description
NM_000400.4(ERCC2):c.2137G>C (p.Gly713Arg) AND Trichothiodystrophy 1, photosensitive
ClinVar Allele ID
31825
ClinVar RefSeq Alternation Syntax
NM_000400.4:c.2137G>C
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
1996-02-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000018276
ClinVar Disease
Trichothiodystrophy 1, photosensitive
Observed Origin Sample
germline
Pubmed
8571952
Drugs