Annotation Detail

Information
Associated Genes
COL1A1
Associated Variants
COL1A1 p.Gly332Arg (p.G332R) ( ENST00000225964.10 )
COL1A1 p.Gly332Arg (p.G332R) ( ENST00000225964.10 )
Associated Disease
Osteogenesis imperfecta type III
Source Database
ClinVar
Description
NM_000088.4(COL1A1):c.994G>A (p.Gly332Arg) AND Osteogenesis imperfecta type III
ClinVar Allele ID
32351
ClinVar RefSeq Alternation Syntax
NM_000088.4:c.994G>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
1996-01-11
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000018853
ClinVar Disease
Osteogenesis imperfecta type III
Observed Origin Sample
germline
Pubmed
2037280
Pubmed
8669434
Drugs