Annotation Detail

Information
Associated Genes
COL1A1 LOC126862586
Associated Variants
COL1A1 p.Gly263Arg (p.G263R) ( ENST00000225964.10 )
COL1A1 p.Gly263Arg (p.G263R) ( ENST00000225964.10 )
Associated Disease
osteogenesis imperfecta
Source Database
ClinVar
Description
NM_000088.4(COL1A1):c.787G>A (p.Gly263Arg) AND Osteogenesis imperfecta
ClinVar Allele ID
32355
ClinVar RefSeq Alternation Syntax
NM_000088.4:c.787G>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
1986-07-05
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000018857
ClinVar Disease
Osteogenesis imperfecta
Observed Origin Sample
germline
Pubmed
1137656
Pubmed
3722186
Drugs