Annotation Detail

Information
Associated Genes
COL1A1
Associated Variants
COL1A1 p.Gly1040Ser (p.G1040S) ( ENST00000225964.10 )
COL1A1 p.Gly1040Ser (p.G1040S) ( ENST00000225964.10 )
Associated Disease
Osteogenesis imperfecta type III
Source Database
ClinVar
Description
NM_000088.4(COL1A1):c.3118G>A (p.Gly1040Ser) AND Osteogenesis imperfecta type III
ClinVar Allele ID
32369
ClinVar RefSeq Alternation Syntax
NM_000088.4:c.3118G>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2022-05-22
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000018871
ClinVar Disease
Osteogenesis imperfecta type III
Observed Origin Sample
germline
Observed Origin Sample
unknown
Pubmed
7789952
Drugs