Annotation Detail

Information
Associated Genes
CAPN3
Associated Variants
CAPN3 p.Trp360Cys (p.W360C) ( ENST00000397163.8, ENST00000357568.8, ENST00000318023.11, ENST00000349748.8 )
CAPN3 p.Trp360Cys (p.W360C) ( ENST00000397163.8, ENST00000318023.11, ENST00000349748.8, ENST00000357568.8 )
Associated Disease
autosomal recessive limb-girdle muscular dystrophy type 2A
Source Database
ClinVar
Description
NM_000070.3(CAPN3):c.1080G>C (p.Trp360Cys) AND Autosomal recessive limb-girdle muscular dystrophy type 2A
ClinVar Allele ID
32658
ClinVar RefSeq Alternation Syntax
NM_000070.3:c.1080G>C
ClinVar RefSeq Alternation Syntax
NM_173087.2:c.936G>C
ClinVar RefSeq Alternation Syntax
NM_024344.2:c.1080G>C
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
1998-11-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000019186
ClinVar Disease
Autosomal recessive limb-girdle muscular dystrophy type 2A
Observed Origin Sample
germline
Pubmed
9771675
Drugs