Annotation Detail

Information
Associated Genes
CLCN1
Associated Variants
CLCN1 p.Gly777AlafsTer17 (p.G777Afs*17) ( ENST00000343257.7, ENST00000650516.2 )
CLCN1 p.Gly777AlafsTer17 (p.G777Afs*17) ( ENST00000343257.7, ENST00000650516.2 )
Associated Disease
Batten-Turner congenital myopathy
Source Database
ClinVar
Description
NM_000083.3(CLCN1):c.2330del (p.Gly777fs) AND Batten-Turner congenital myopathy
ClinVar Allele ID
33894
ClinVar RefSeq Alternation Syntax
NR_046453.2:n.2285del
ClinVar RefSeq Alternation Syntax
NM_000083.3:c.2330del
Clinical Significance Description
not provided
Clinical Significance Review Status
no assertion provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000020105
ClinVar Disease
Batten-Turner congenital myopathy
Observed Origin Sample
unknown
Drugs