Annotation Detail

Information
Associated Genes
NTRK1
Associated Variants
NTRK1 p.Arg554GlyfsTer104 (p.R554Gfs*104) ( ENST00000358660.3, ENST00000368196.7, ENST00000392302.7, ENST00000524377.7, ENST00000674537.2 )
NTRK1 p.Arg554GlyfsTer104 (p.R554Gfs*104) ( ENST00000358660.3, ENST00000368196.7, ENST00000392302.7, ENST00000524377.7, ENST00000674537.2 )
Associated Disease
Hereditary insensitivity to pain with anhidrosis
Source Database
ClinVar
Description
NM_002529.4(NTRK1):c.1660del (p.Arg554fs) AND Hereditary insensitivity to pain with anhidrosis
ClinVar Allele ID
34157
ClinVar RefSeq Alternation Syntax
NM_002529.4:c.1660del
ClinVar RefSeq Alternation Syntax
NM_001007792.1:c.1552del
ClinVar RefSeq Alternation Syntax
NM_001012331.2:c.1642del
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2023-09-28
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000020468
ClinVar Disease
Hereditary insensitivity to pain with anhidrosis
Observed Origin Sample
germline
Pubmed
10982191
Pubmed
11071380
Pubmed
11748840
Drugs