Annotation Detail

Information
Associated Genes
COL1A1
Associated Variants
COL1A1 p.Gly809AlafsTer299 (p.G809Afs*299) ( ENST00000225964.10 )
COL1A1 p.Gly809AlafsTer299 (p.G809Afs*299) ( ENST00000225964.10 )
Associated Disease
osteogenesis imperfecta
Source Database
ClinVar
Description
NM_000088.4(COL1A1):c.2418del (p.Gly809fs) AND Osteogenesis imperfecta
ClinVar Allele ID
44575
ClinVar RefSeq Alternation Syntax
NM_000088.4:c.2418del
Clinical Significance Description
Likely pathogenic
Clinical Significance Last Update
2011-08-18
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000029566
ClinVar Disease
Osteogenesis imperfecta
Observed Origin Sample
germline
Drugs