Annotation Detail

Information
Associated Genes
G6PC1
Associated Variants
G6PC1 p.Gln27ArgfsTer9 (p.Q27Rfs*9) ( ENST00000253801.7, ENST00000592383.5, ENST00000585489.1 )
G6PC1 p.Gln27ArgfsTer9 (p.Q27Rfs*9) ( ENST00000253801.7, ENST00000585489.1, ENST00000592383.5 )
Associated Disease
not provided
Source Database
ClinVar
Description
NM_000151.4(G6PC1):c.79del (p.Gln27fs) AND not provided
ClinVar Allele ID
33914
ClinVar RefSeq Alternation Syntax
NM_001270397.2:c.79del
ClinVar RefSeq Alternation Syntax
NM_000151.4:c.79del
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2023-05-01
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000199426
ClinVar Disease
not provided
Observed Origin Sample
germline
Drugs