Annotation Detail

Information
Associated Genes
CLCN1
Associated Variants
CLCN1 p.Gln552Arg (p.Q552R) ( ENST00000343257.7, ENST00000650516.2 )
CLCN1 p.Gln552Arg (p.Q552R) ( ENST00000343257.7, ENST00000650516.2 )
Associated Disease
not provided
Source Database
ClinVar
Description
NM_000083.3(CLCN1):c.1655A>G (p.Gln552Arg) AND not provided
ClinVar Allele ID
32577
ClinVar RefSeq Alternation Syntax
NR_046453.2:n.1610A>G
ClinVar RefSeq Alternation Syntax
NM_000083.3:c.1655A>G
Clinical Significance Description
Pathogenic/Likely pathogenic
Clinical Significance Last Update
2023-05-17
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000498537
ClinVar Disease
not provided
Observed Origin Sample
germline
Observed Origin Sample
unknown
Drugs