Annotation Detail

Information
Associated Genes
ERCC2
Associated Variants
ERCC2 p.Arg683Trp (p.R683W) ( ENST00000391944.8, ENST00000391945.10, ENST00000684407.1 )
ERCC2 p.Arg683Trp (p.R683W) ( ENST00000391944.8, ENST00000391945.10, ENST00000684407.1 )
Associated Disease
Inborn genetic diseases
Source Database
ClinVar
Description
NM_000400.4(ERCC2):c.2047C>T (p.Arg683Trp) AND Inborn genetic diseases
ClinVar Allele ID
31832
ClinVar RefSeq Alternation Syntax
NM_000400.4:c.2047C>T
Clinical Significance Description
Likely pathogenic
Clinical Significance Last Update
2017-02-08
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000623275
ClinVar Disease
Inborn genetic diseases
Observed Origin Sample
germline
Drugs