Annotation Detail

Information
Associated Genes
G6PC1
Associated Variants
G6PC1 p.Leu216= (p.L216=) ( ENST00000592383.5, ENST00000253801.7, ENST00000585489.1 )
G6PC1 p.Leu216= (p.L216=) ( ENST00000253801.7, ENST00000585489.1, ENST00000592383.5 )
Associated Disease
not provided
Source Database
ClinVar
Description
NM_000151.4(G6PC1):c.648G>T (p.Leu216=) AND not provided
ClinVar Allele ID
27042
ClinVar RefSeq Alternation Syntax
NM_001270397.2:c.*40G>T
ClinVar RefSeq Alternation Syntax
NM_000151.4:c.648G>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2022-04-11
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000723833
ClinVar Disease
not provided
Observed Origin Sample
germline
Drugs