Annotation Detail

Information
Associated Genes
PTCH1 LOC100507346
Associated Variants
PTCH1 p.Leu664ArgfsTer27 (p.L664Rfs*27) ( ENST00000331920.11, ENST00000429896.6, ENST00000430669.6, ENST00000437951.6, ENST00000692981.1, ENST00000711046.1 )
PTCH1 p.Leu664ArgfsTer27 (p.L664Rfs*27) ( ENST00000331920.11, ENST00000429896.6, ENST00000430669.6, ENST00000437951.6, ENST00000692981.1, ENST00000711046.1 )
Associated Disease
Congenital hydrocephalus
Source Database
ClinVar
Description
NM_000264.5(PTCH1):c.1991_1997del (p.Leu664fs) AND Congenital hydrocephalus
ClinVar Allele ID
672255
ClinVar RefSeq Alternation Syntax
NR_149061.2:n.2896_2902del
ClinVar RefSeq Alternation Syntax
NM_001083606.3:c.1538_1544del
ClinVar RefSeq Alternation Syntax
NM_000264.5:c.1991_1997del
ClinVar RefSeq Alternation Syntax
NM_001083603.3:c.1988_1994del
ClinVar RefSeq Alternation Syntax
NR_038982.1:n.943_949del
ClinVar RefSeq Alternation Syntax
NM_001354918.2:c.1835_1841del
ClinVar RefSeq Alternation Syntax
NM_001083604.3:c.1538_1544del
ClinVar RefSeq Alternation Syntax
NM_001083605.3:c.1538_1544del
ClinVar RefSeq Alternation Syntax
NM_001083602.3:c.1793_1799del
ClinVar RefSeq Alternation Syntax
NM_001083607.3:c.1538_1544del
Clinical Significance Description
Likely pathogenic
Clinical Significance Last Update
2018-07-05
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000845213
ClinVar Disease
Congenital hydrocephalus
Observed Origin Sample
germline
Drugs