Annotation Detail

Information
Associated Genes
DES
Associated Variants
DES p.Ser12Phe (p.S12F) ( ENST00000373960.4 )
DES p.Ser12Phe (p.S12F) ( ENST00000373960.4 )
Associated Disease
Desmin-related myofibrillar myopathy
Source Database
ClinVar
Description
NM_001927.4(DES):c.35C>T (p.Ser12Phe) AND Desmin-related myofibrillar myopathy
ClinVar Allele ID
77309
ClinVar RefSeq Alternation Syntax
NM_001927.4:c.35C>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2021-02-16
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV001061421
ClinVar Disease
Desmin-related myofibrillar myopathy
Observed Origin Sample
germline
Drugs