Annotation Detail

Information
Associated Genes
KRT5
Associated Variants
KRT5 p.Pro25Leu (p.P25L) ( ENST00000252242.9 )
KRT5 p.Pro25Leu (p.P25L) ( ENST00000252242.9 )
Associated Disease
epidermolysis bullosa simplex
Source Database
ClinVar
Description
NM_000424.4(KRT5):c.74C>T (p.Pro25Leu) AND Epidermolysis bullosa simplex
ClinVar Allele ID
29687
ClinVar RefSeq Alternation Syntax
NM_000424.4:c.74C>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2018-02-26
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV001352721
ClinVar Disease
Epidermolysis bullosa simplex
Observed Origin Sample
germline
Observed Origin Sample
de novo
Drugs