Annotation Detail

Information
Associated Genes
G6PC1
Associated Variants
G6PC1 p.Gln27ArgfsTer9 (p.Q27Rfs*9) ( ENST00000253801.7, ENST00000592383.5, ENST00000585489.1 )
G6PC1 p.Gln27ArgfsTer9 (p.Q27Rfs*9) ( ENST00000253801.7, ENST00000585489.1, ENST00000592383.5 )
Associated Disease
Glycogen storage disease, type I
Source Database
ClinVar
Description
NM_000151.4(G6PC1):c.79del (p.Gln27fs) AND Glycogen storage disease, type I
ClinVar Allele ID
33914
ClinVar RefSeq Alternation Syntax
NM_001270397.2:c.79del
ClinVar RefSeq Alternation Syntax
NM_000151.4:c.79del
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2020-06-25
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV001449697
ClinVar Disease
Glycogen storage disease, type I
Observed Origin Sample
germline
Drugs