Annotation Detail

Information
Associated Genes
ACVRL1
Associated Variants
ACVRL1 p.Trp399Ser (p.W399S) ( ENST00000713619.1, ENST00000552678.2, ENST00000547400.6, ENST00000551576.6, ENST00000550683.5, ENST00000388922.9, ENST00000419526.6 )
ACVRL1 p.Trp399Ser (p.W399S) ( ENST00000388922.9, ENST00000419526.6, ENST00000547400.6, ENST00000550683.5, ENST00000551576.6, ENST00000552678.2, ENST00000713619.1 )
Source Database
ClinVar
Description
NM_000020.3(ACVRL1):c.1196G>C (p.Trp399Ser) AND Cardiovascular phenotype
ClinVar Allele ID
23294
ClinVar RefSeq Alternation Syntax
NM_001077401.2:c.1196G>C
ClinVar RefSeq Alternation Syntax
NM_000020.3:c.1196G>C
Clinical Significance Description
Likely pathogenic
Clinical Significance Last Update
2019-08-22
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV002345234
Observed Origin Sample
germline
Drugs