Annotation Detail

Information
Associated Genes
COL1A1
Associated Variants
COL1A1 p.Gly605AlafsTer161 (p.G605Afs*161) ( ENST00000225964.10 )
COL1A1 p.Gly605AlafsTer161 (p.G605Afs*161) ( ENST00000225964.10 )
Associated Disease
Osteogenesis imperfecta type III
Source Database
ClinVar
Description
NM_000088.4(COL1A1):c.1812del (p.Gly605fs) AND Osteogenesis imperfecta type III
ClinVar Allele ID
44569
ClinVar RefSeq Alternation Syntax
NM_000088.4:c.1812del
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2021-05-06
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV002470719
ClinVar Disease
Osteogenesis imperfecta type III
Observed Origin Sample
germline
Drugs