Annotation Detail

Information
Associated Genes
ERCC2
Associated Variants
ERCC2 p.Ala717Gly (p.A717G) ( ENST00000391944.8, ENST00000391945.10, ENST00000684407.1 )
ERCC2 p.Ala717Gly (p.A717G) ( ENST00000391944.8, ENST00000391945.10, ENST00000684407.1 )
Associated Disease
xeroderma pigmentosum
Source Database
ClinVar
Description
NM_000400.4(ERCC2):c.2150C>G (p.Ala717Gly) AND Xeroderma pigmentosum
ClinVar Allele ID
137841
ClinVar RefSeq Alternation Syntax
NM_000400.4:c.2150C>G
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2023-01-04
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV003114266
ClinVar Disease
Xeroderma pigmentosum
Observed Origin Sample
germline
Drugs