Annotation Detail

Information
Associated Genes
CLCN1
Associated Variants
CLCN1 p.Thr550Met (p.T550M) ( ENST00000343257.7, ENST00000650516.2 )
CLCN1 p.Thr550Met (p.T550M) ( ENST00000343257.7, ENST00000650516.2 )
Associated Disease
not provided
Source Database
ClinVar
Description
NM_000083.3(CLCN1):c.1649C>T (p.Thr550Met) AND not provided
ClinVar Allele ID
204363
ClinVar RefSeq Alternation Syntax
NM_000083.3:c.1649C>T
ClinVar RefSeq Alternation Syntax
NR_046453.2:n.1604C>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2023-07-01
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV003326370
ClinVar Disease
not provided
Observed Origin Sample
germline
Drugs