Annotation Detail

Information
Associated Genes
CLCN1
Associated Variants
CLCN1 p.Arg338Gln (p.R338Q) ( ENST00000343257.7, ENST00000650516.2 )
CLCN1 p.Arg338Gln (p.R338Q) ( ENST00000343257.7, ENST00000650516.2 )
Associated Disease
CLCN1-related disorder
Source Database
ClinVar
Description
NM_000083.3(CLCN1):c.1013G>A (p.Arg338Gln) AND CLCN1-related disorder
ClinVar Allele ID
33889
ClinVar RefSeq Alternation Syntax
NM_000083.3:c.1013G>A
ClinVar RefSeq Alternation Syntax
NR_046453.2:n.1118G>A
Clinical Significance Description
Pathogenic
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV003335049
ClinVar Disease
CLCN1-related disorder
Observed Origin Sample
germline
Drugs