Annotation Detail

Information
Associated Genes
MSH2
Associated Variants
MSH2 p.Gln493Ter (p.Q493*) ( ENST00000233146.7, ENST00000406134.5, ENST00000543555.6, ENST00000645506.1, ENST00000713854.1, ENST00000713919.1 )
MSH2 p.Gln493Ter (p.Q493*) ( ENST00000233146.7, ENST00000406134.5, ENST00000543555.6, ENST00000645506.1, ENST00000713854.1, ENST00000713919.1 )
Associated Disease
Lynch syndrome 1
Source Database
ClinVar
Description
NM_000251.3(MSH2):c.1477C>T (p.Gln493Ter) AND Lynch syndrome 1
ClinVar Allele ID
96152
ClinVar RefSeq Alternation Syntax
NM_000251.3:c.1477C>T
ClinVar RefSeq Alternation Syntax
NM_001258281.1:c.1279C>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2023-08-02
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV003452836
ClinVar Disease
Lynch syndrome 1
Observed Origin Sample
unknown
Drugs