Annotation Detail

Information
Associated Genes
TYR
Associated Variants
TYR p.Arg299His (p.R299H) ( ENST00000263321.6 )
TYR p.Arg299His (p.R299H) ( ENST00000263321.6 )
Associated Disease
Tyrosinase-negative oculocutaneous albinism Oculocutaneous albinism type 1B
Source Database
ClinVar
Description
NM_000372.5(TYR):c.896G>A (p.Arg299His) AND multiple conditions
ClinVar Allele ID
18835
ClinVar RefSeq Alternation Syntax
NM_000372.5:c.896G>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2023-10-31
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV003488321
ClinVar Disease
Oculocutaneous albinism type 1B
ClinVar Disease
Tyrosinase-negative oculocutaneous albinism
Observed Origin Sample
unknown
Drugs