Annotation Detail

Information
Associated Genes
TBCD ZNF750
Associated Variants
TBCD c.1318+16693G>A, ZNF750 p.Tyr276= (p.Y276=) ( ENST00000684544.1, ENST00000684429.1, ENST00000684760.1, ENST00000683282.1, ENST00000269394.4, ENST00000539345.6, ENST00000682479.1, ENST00000684188.1, ENST00000572562.1, ENST00000684408.1, ENST00000682722.1, ENST00000684464.1, ENST00000684349.1, ENST00000684000.1, ENST00000355528.9, ENST00000683821.1 )
TBCD c.1318+16693G>A, ZNF750 p.Tyr276= (p.Y276=) ( ENST00000355528.9, ENST00000539345.6, ENST00000682479.1, ENST00000682722.1, ENST00000683282.1, ENST00000683821.1, ENST00000684000.1, ENST00000684188.1, ENST00000684349.1, ENST00000684408.1, ENST00000684429.1, ENST00000684464.1, ENST00000684544.1, ENST00000684760.1, ENST00000269394.4, ENST00000572562.1 )
Associated Disease
ZNF750-related disorder
Source Database
ClinVar
Description
NM_024702.3(ZNF750):c.828C>T (p.Tyr276=) AND ZNF750-related disorder
ClinVar Allele ID
3220654
ClinVar RefSeq Alternation Syntax
NM_001411102.1:c.1318+16693G>A
ClinVar RefSeq Alternation Syntax
NM_024702.3:c.828C>T
ClinVar RefSeq Alternation Syntax
NM_005993.5:c.1318+16693G>A
ClinVar RefSeq Alternation Syntax
NM_001411101.1:c.1267+16693G>A
Clinical Significance Description
Likely benign
Clinical Significance Last Update
2019-05-02
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV003978965
ClinVar Disease
ZNF750-related disorder
Observed Origin Sample
germline
Drugs