Annotation Detail

Information
Associated Genes
ACVRL1
Associated Variants
ACVRL1 p.Arg374Trp (p.R374W) ( ENST00000388922.9, ENST00000550683.5, ENST00000419526.6, ENST00000713619.1, ENST00000552678.2, ENST00000547400.6, ENST00000551576.6 )
ACVRL1 p.Arg374Trp (p.R374W) ( ENST00000388922.9, ENST00000419526.6, ENST00000547400.6, ENST00000550683.5, ENST00000551576.6, ENST00000552678.2, ENST00000713619.1 )
Associated Disease
ACVRL1-related disorder
Source Database
ClinVar
Description
NM_000020.3(ACVRL1):c.1120C>T (p.Arg374Trp) AND ACVRL1-related disorder
ClinVar Allele ID
23288
ClinVar RefSeq Alternation Syntax
NM_001077401.2:c.1120C>T
ClinVar RefSeq Alternation Syntax
NM_000020.3:c.1120C>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2023-09-21
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV004547469
ClinVar Disease
ACVRL1-related disorder
Observed Origin Sample
germline
Drugs