Annotation Detail

Information
Associated Genes
ERCC2
Associated Variants
ERCC2 p.Asp681Asn (p.D681N) ( ENST00000391944.8, ENST00000391945.10, ENST00000684407.1 )
ERCC2 p.Arg616Trp (p.R616W) ( ENST00000391944.8, ENST00000391945.10, ENST00000684407.1 )
ERCC2 p.Asp681Asn (p.D681N) ( ENST00000391944.8, ENST00000391945.10, ENST00000684407.1 )
ERCC2 p.Arg616Trp (p.R616W) ( ENST00000391944.8, ENST00000391945.10, ENST00000684407.1 )
Associated Disease
cerebrooculofacioskeletal syndrome 1
Source Database
DisGeNET
Description
Here we report the first involvement of the XPD gene in a new case of UV-sensitive COFS syndrome, with heterozygous substitutions-a R616W null mutation (previously seen in patients in XP complementation group D) and a unique D681N mutation-demonstrating that a third gene can be involved in COFS syndrome.
Pubmed
11443545
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.240542883744161
Year of publication
2001
Drugs