Annotation Detail

Information
Associated Genes
ERCC2
Associated Variants
ERCC2 p.Arg722Trp (p.R722W) ( ENST00000391944.8, ENST00000391945.10, ENST00000684407.1 )
ERCC2 p.Arg722Trp (p.R722W) ( ENST00000391944.8, ENST00000391945.10, ENST00000684407.1 )
Associated Disease
Trichothiodystrophy Syndromes
Source Database
DisGeNET
Description
Patient TTD24PV was compound heterozygous for a typical TTD allele (c.2164C>T, p.Arg722Trp) and for a new XPD allele with a mutation that partially affects intron 10 splicing, resulting in both mutated and normal XPD transcripts (that together represent 15% of the total XPD mRNA).
Pubmed
19085937
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.1379151635573
Year of publication
2009
Drugs