Annotation Detail

Information
Associated Genes
TRPS1
Associated Variants
TRPS1 MUTATION
TRPS1 MUTATION
Associated Disease
Langer-Giedion syndrome
Source Database
DisGeNET
Description
In the March issue of the Journal in 2012, we reported on a girl with Langer-Giedion syndrome (LGS) phenotype and a 7.5 Mb interstitial deletion at 8q23.3q24.13, encompassing the EXT1, but not the TRPS1 gene.
Pubmed
25899858
Section of the abstract supporting the evidence
ALL_TEXT_1/3
Number of the section of the abstract supporting the evidence
1
Number of the sentence supporting the evidence
1
Original source reporting the Gene Disease association
BeFree,CTD_human,ORPHANET
DisGENET score for the Gene Disease association
0.242171534976642
Drugs