Annotation Detail

Information
Associated Genes
G6PC1
Associated Variants
G6PC1 p.Arg83His (p.R83H) ( ENST00000592383.5, ENST00000253801.7, ENST00000585489.1 )
G6PC1 p.Arg170Ter (p.R170*) ( ENST00000253801.7, ENST00000592383.5, ENST00000585489.1 )
G6PC1 p.Arg83His (p.R83H) ( ENST00000592383.5, ENST00000253801.7, ENST00000585489.1 )
G6PC1 p.Arg170Ter (p.R170*) ( ENST00000253801.7, ENST00000585489.1, ENST00000592383.5 )
Associated Disease
Glycogen Storage Disease Type I
Source Database
DisGeNET
Description
Our findings suggest that a screening for the g727t, R170X, and R83H mutations by simple DNA-based diagnostic methods can detect 95% of the G6Pase mutant alleles in Japanese patients with GSD-Ia, and remaining mutations can be identified and characterized by the direct sequencing of genomic DNA and/or the analysis of ectopically expressed mRNA.
Pubmed
10748407
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.45486328961596
Year of publication
2000
Drugs