Annotation Detail

Information
Associated Genes
CYP11B1
Associated Variants
CYP11B1 p.Arg448His (p.R448H) ( ENST00000292427.10, ENST00000377675.3, ENST00000517471.5 )
CYP11B1 p.Arg448His (p.R448H) ( ENST00000292427.10, ENST00000377675.3, ENST00000517471.5 )
Associated Disease
Congenital adrenal hyperplasia due to 11-Beta-hydroxylase deficiency
Source Database
DisGeNET
Description
Steroid 11-beta hydroxylase deficiency caused by compound heterozygosity for a novel mutation in intron 7 (IVS 7 DS+4A to G) in one CYP11B1 allele and R448H in exon 8 in the other.
Pubmed
20024693
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.487871814290329
Year of publication
2010
Drugs