Annotation Detail

Information
Associated Genes
CLASP1 RNU4ATAC
Associated Variants
CLASP1 c.196-604C>T ( ENST00000263710.8, ENST00000409078.8, ENST00000455322.7, ENST00000541377.5, ENST00000696935.1, ENST00000700754.1, ENST00000700755.1 )
CLASP1 c.196-604C>T ( ENST00000263710.8, ENST00000409078.8, ENST00000455322.7, ENST00000541377.5, ENST00000696935.1, ENST00000700754.1, ENST00000700755.1 )
Associated Disease
Osteodysplastic primordial dwarfism, type 1
Source Database
ClinVar
Description
NM_001395891.1(CLASP1):c.196-604C>T AND Osteodysplastic primordial dwarfism, type 1
ClinVar Allele ID
39140
ClinVar RefSeq Alternation Syntax
NM_001395891.1:c.196-604C>T
ClinVar RefSeq Alternation Syntax
NM_015282.3:c.196-604C>T
ClinVar RefSeq Alternation Syntax
NM_001378003.1:c.196-604C>T
ClinVar RefSeq Alternation Syntax
NM_001142274.2:c.196-604C>T
ClinVar RefSeq Alternation Syntax
NM_001378005.1:c.196-604C>T
ClinVar RefSeq Alternation Syntax
NM_001378004.1:c.196-604C>T
ClinVar RefSeq Alternation Syntax
NM_001142273.2:c.196-604C>T
ClinVar RefSeq Alternation Syntax
NR_023343.1:n.50G>A
ClinVar RefSeq Alternation Syntax
NM_001207051.2:c.196-604C>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2011-04-08
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000023102
ClinVar Disease
Osteodysplastic primordial dwarfism, type 1
Observed Origin Sample
germline
Observed Origin Sample
unknown
Pubmed
21474761
Drugs