Annotation Detail

Information
Associated Genes
TERT LOC110806263
Associated Variants
TERT p.Leu50= (p.L50=) ( ENST00000334602.10, ENST00000310581.10 )
TERT p.Leu50= (p.L50=) ( ENST00000310581.10, ENST00000334602.10 )
Associated Disease
acute myeloid leukemia Dyskeratosis congenita, autosomal dominant 1 aplastic anemia Pulmonary fibrosis and/or bone marrow failure, Telomere-related, 1 Dyskeratosis congenita, autosomal dominant 2 interstitial lung disease 2 Melanoma, cutaneous malignant, susceptibility to, 9
Source Database
ClinVar
Description
NM_198253.3(TERT):c.150G>A (p.Leu50=) AND multiple conditions
ClinVar Allele ID
273563
ClinVar RefSeq Alternation Syntax
NR_149162.3:n.229G>A
ClinVar RefSeq Alternation Syntax
NM_001193376.3:c.150G>A
ClinVar RefSeq Alternation Syntax
NR_149163.3:n.229G>A
ClinVar RefSeq Alternation Syntax
NM_198253.3:c.150G>A
Clinical Significance Description
Uncertain significance
Clinical Significance Last Update
2018-10-31
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000764569
ClinVar Disease
Aplastic anemia
ClinVar Disease
Dyskeratosis congenita, autosomal dominant 2
ClinVar Disease
Pulmonary fibrosis and/or bone marrow failure, Telomere-related, 1
ClinVar Disease
Dyskeratosis congenita, autosomal dominant 1
ClinVar Disease
Acute myeloid leukemia
ClinVar Disease
Interstitial lung disease 2
ClinVar Disease
Melanoma, cutaneous malignant, susceptibility to, 9
Observed Origin Sample
unknown
Drugs